The clinical findings in DEEC are: Disproportionate dwarfisms (with short spine, kyphoscoliosis, pectus carinatus), genu valgum, etc. The epiphyses are poorly ossified and deformed. Progressive motor weakness may be the first clinical symptom of spinal cord compression caused by a kyphoscoliosis. In these cases we must make a differential diagnosis with a premature osteoarthritis of the hips. We report two cases. One of them was treated with spinal fusion for correction of her kyphoscoliosis, andthe other one with a total hip arthroplasty.

The clinical findings in DEEC are: Disproportionate dwarfisms (with short spine, kyphoscoliosis, pectus carinatus), genu valgum, etc. The epiphyses are poorly ossified and deformed. Progressive motor weakness may be the first clinical symptom of spinal cord compression caused by a kyphoscoliosis. In these cases we must make a differential diagnosis with a premature osteoarthritis of the hips. We report two cases. One of them was treated with spinal fusion for correction of her kyphoscoliosis, andthe other one with a total hip arthroplasty.